RECOMMENDATIONS FOR DIAGNOSIS AND MANAGEMENT OF IDIOPATHIC PULMONARY FIBROSIS 2017

LIETUVOS PULMONOLOGŲ IR ALERGOLOGŲ DRAUGIJA, LIETUVOS RADIOLOGŲ ASOCIACIJA, LIETUVOS PATOLOGŲ DRAUGIJA

  • Kęstutis Malakauskas
  • Kristina Biekšienė
  • Laima Dobrovolskienė
  • Skaidrius Miliauskas
  • Valdas Šarauskas
  • Jurgita Zaveckienė
  • Marius Žemaitis
Keywords: idiopatic pulmonary fibrosis, diagnosis, management

Abstract

Idiopathic pulmonary fibrosis (IPF) IPF is a specific form of chronic, progressive fibrosing interstitial pneumonia of unknown cause occurring in adults. The incidence has been rising in recent years probably due to improved diagnostic methods and increased life expectancy du to disease-modifying therapy. Novel antifibrotic drugs as nintedanib and pirfenidone that slow disease progression are now available. In current recommendations diagnostic aspects, pharmacological and non-pharmacological management of IPF are presented.

Author Biographies

Kęstutis Malakauskas

Department of Pulmonology, Medical Academy, Lithuanian University of Health Sciences

Kristina Biekšienė

Department of Pulmonology, Medical Academy, Lithuanian University of Health Sciences

Laima Dobrovolskienė

Department of Radiology, Medical Academy, Lithuanian University of Health Sciences

Skaidrius Miliauskas

Department of Pulmonology, Medical Academy, Lithuanian University of Health Sciences

Valdas Šarauskas

Department of Pathological anatomy, Medical Academy, Lithuanian University of Health Sciences

Jurgita Zaveckienė

Department of Radiology, Medical Academy, Lithuanian University of Health Sciences

Marius Žemaitis

Department of Pulmonology, Medical Academy, Lithuanian University of Health Sciences

How to Cite
1.
Malakauskas K, Biekšienė K, Dobrovolskienė L, Miliauskas S, Šarauskas V, Zaveckienė J, Žemaitis M. RECOMMENDATIONS FOR DIAGNOSIS AND MANAGEMENT OF IDIOPATHIC PULMONARY FIBROSIS 2017 [Internet]. PIA 2017 Sep.;1(2):83-91.[cited 2024 May 19 ] Available from: http://pia.pulmoalerg.lt/index.php/PIA/article/view/207